bleach vs mad deer disease

it's deer hunting season, and the bad news is that some deer in the USA are affected with Chronic wasting disease, caused by a prion that is similar to the mad cow disease (vCJD) that was found in the UK several years ago.

the prion family of neurological disease has variations that affect many animals: not all are infectious to humans.

To date, about 260 cases of vCJD, mostly in the United Kingdom, have been reported related to consuming beef but none in which the disease was acquired in the U.S.

Other TSEs are found in specific kinds of animals. These include BSE, mink encephalopathy, feline encephalopathy, and scrapie, which affects sheep and goats. Chronic wasting disease (CWD) affects elk and deer and is increasingly prevalent in certain areas in the United States. To date no transmission of CWD to humans has been reported. top

there are now reports that bleach might stop the spread by deactivating, but not killing, the prion of CWD LINK

Bleach isn’t the cure-all for CWD. It only works on nonporous surfaces, but it’s the first thing scientists have discovered that inactivates the abnormal prion that’s wreaking havoc on cervid herds. What’s more, we know the concentration and exposure time for bleach to be effective. And it works any time, today or in three weeks, because, unfortunately, the prions don’t disappear.

Chronic wasting disease in deer/elk has been spreading in the USA.

CWD is affecting many deer and elk in the USA... and some worry it will cross the species barrier to infect humans similar to how mad cow disease spread to humans (who ate brain/nerve tissue in meat from the infected cows).

so if you are a deer hunter in an area where there is CWD, how do you butcher the meat?

so far there has not been proof it spreads to humans, but macaq monkeys and squirrels might be able to be infected.  link2

and there have been cases from eating squirrels in the USA.

In 1997, a number of people from Kentucky developed vCJD. It was discovered that all had consumed squirrel brains, although a coincidental relationship between the disease and this dietary practice may have been involved.^[39]

LiveScience report on a case in NewYork state also associated with eating squirrel.

So is there a link between CWD in deer and CJD in humans?

Creutzfeldt–Jakob_disease

CJD is caused by a protein known as a prion.^[5] Infectious prions are misfolded proteins that can cause normally folded proteins to become misfolded.^[4] Most cases occur spontaneously, while about 7.5% of cases are inherited from a person's parents in an autosomal dominant manner.^[4] Exposure to brain or spinal tissue from an infected person may also result in spread.^[4] There is no evidence that it can spread between people via normal contact or blood transfusions.^[4] 

translation: You can't get regular CJD easily from contact with a patient with that disease (unless you are incontact with infected tissue/blood), but that might not be true in the variant version (vCJD) aka mad cow disease.

,
,,the mad cow disease that affected humans in the UK was called Varient CJD (wikipedia) from eating beef contaminated with brain/nerve tissue and also from blood transfusions if the donor had the infectious prions in their blood.

the good news: Not everyone who was infected got the disease: there is a genetic link to whether or not you were susceptible.

the bad news: it could take up to 50 years to develop the disease.

In New Guinea, a disease Kuru was known to be caused by cannibalism, where the family ate part of the brain of the dead: forbidding the practice was thought to have eliminated it, but now there have been new cases reported. Were these new cases from a long latent period, with the disease appearing 50 years later from modern mortuary practice, or from secretly continuing the practice?